Langerhan’s Cell Histiocytosis of Right scapular Bone: a case report

نویسندگان

  • Ho-En Tung
  • SHin-Lin SHiH
  • FEi-SHiH Yang
چکیده

Reported here is a case of Langerhan’s cell histiocytosis (LCH), which occurred to a 1-year-old boy presented init ial ly with fever and rightshoulder swelling. In this case, plain radiography and CT revealed an ill-defined osteolytic lesion associated with surrounding soft tissue mass in the right glenoid area. The boy underwent debridement and the specimens were seen to be involved by the Langerhan’s cell microscopically. Vertebra plana was found at L2 vertebra after long bone survey. Langerhan’s cell histiocytosis (LCH) can occur to individuals of any age, but most commonly to children with a slight male predominance. It was previously called histiocytosis X and defined as an abnormal proliferation of the Langerhan’s cells in various organs or tissues [1]. The reticuloendothelial system (i.e., bones, skin, lymph nodes, liver, and spleen) is involved in most cases, and osseous involvement is the most common manifestation [2]. To our knowledge, a scapular lesion has rarely been found as the initial presentation of LCH. Based on the boy’s clinical history and his presentation at this time, the case may easily be mistaken as a case of osteomyelitis.

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تاریخ انتشار 2007